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Article Dans Une Revue Revue du Praticien (La) Année : 2015

[Congenital haemorrhagic diseases].

Résumé

Congenital haemorrhagic diseases are the consequences of haemostasis dysfunction or defects. Among primary haemostasis disorders, von Willebrand disease is the most frequent. Hopefully the type 1 von Willebrand disease, which affects 85% of patients, is generally a mild haemorrhagic disorder. However it may induce some troubles during the everyday life. On the other side, haemophilia is the most frequent congenital coagulation disorders. Haemophilia A is due a factor VIII deficiency while haemophilia B is due to a factor IX deficiency. Haemophilia is mainly a musculoskeletal disease. Recurrent joint bleedings may lead to a severe disabling arthropathy. The organization of care for hemophilia is managed by haemophilia treatment centers. Other rare bleeding disorders may lead to the same complications but requires specific treatments.

Domaines

Hématologie
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Dates et versions

hal-01975940 , version 1 (09-01-2019)

Identifiants

  • HAL Id : hal-01975940 , version 1
  • PUBMED : 26165091

Citer

Jean-Francois Schved. [Congenital haemorrhagic diseases].. Revue du Praticien (La), 2015, 65 (5), pp.613-7. ⟨hal-01975940⟩

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