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Article Dans Une Revue Revue du Praticien (La) Année : 2015

[Congenital haemorrhagic diseases].


Congenital haemorrhagic diseases are the consequences of haemostasis dysfunction or defects. Among primary haemostasis disorders, von Willebrand disease is the most frequent. Hopefully the type 1 von Willebrand disease, which affects 85% of patients, is generally a mild haemorrhagic disorder. However it may induce some troubles during the everyday life. On the other side, haemophilia is the most frequent congenital coagulation disorders. Haemophilia A is due a factor VIII deficiency while haemophilia B is due to a factor IX deficiency. Haemophilia is mainly a musculoskeletal disease. Recurrent joint bleedings may lead to a severe disabling arthropathy. The organization of care for hemophilia is managed by haemophilia treatment centers. Other rare bleeding disorders may lead to the same complications but requires specific treatments.


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Dates et versions

hal-01975940 , version 1 (09-01-2019)


  • HAL Id : hal-01975940 , version 1
  • PUBMED : 26165091


Jean-Francois Schved. [Congenital haemorrhagic diseases].. Revue du Praticien (La), 2015, 65 (5), pp.613-7. ⟨hal-01975940⟩


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